• Mixture of substrate and internal standard for 50 MS/MS enzyme assay of Galactosylceramidase (GALC).
• Comes with the relevant buffer.
• Comes with qNMR quantified enzymatic product relevant to the GALC assay, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
"Minimum order quantity: 10 vials (500 assays)"
Krabbe
Galactosylceramidase Assay Cocktail
SKU: CS9B
The mixture contains C8 Galactosylceramide (MW: 587.8) and C8 Ceramide-d5 (MW: 430.7)
Catalog Number: CS9B
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- Spacil, Z., Tatipaka, H., Barcenas, M., Scott, C.R., Turecek, F. and Gelb, M.H., 2013. High-throughput assay of 9 lysosomal enzymes for newborn screening. Clinical chemistry, 59(3), pp.502-511.
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