• Mixture of substrate and internal standard for 50 MS/MS enzyme assay of Lysosomal Acid Lipase (LIPA).
 
• Comes with the relevant detergent-containing buffer.
 
• Comes with ethanolic cardiolipin solution required as a LIPA activator.
 
• Comes with qNMR quantified enzymatic product relevant to the LIPA assay, for mass spectrometry tuning and standard curve generation (See Absolute Quantification).
 
• Our LIPA substrate is 100% specific for LIPA; therefore, LIPA assays do not require duplicate assays done in parallel in the presence and absence of the LIPA inactivator Lalistat-2. 
 
               "Minimum order quantity: 5 vials (250 assays)"
Wolman disease; LAL; Lysosomal acid lipase